Brunel University Research Archive(BURA) preserves and enables easy and open access to all
types of digital content. It showcases Brunel's research outputs.
Research contained within BURA is open access, although some publications may be subject
to publisher imposed embargoes. All awarded PhD theses are also archived on BURA.
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| Issue Date | Title | Author(s) |
|---|---|---|
| 2014 | Generation and characterisation of Friedreich ataxia YG8R mouse fibroblast and neural stem cell models | Sandi, C; Sandi, M; Jassal, H; Ezzatizadeh, V; Anjomani-Virmouni, S; Al-Mahdawi, S; Pook, MA |
| 2015 | Characterization of the retinal pigment epithelium in Friedreich ataxia | Crombie, DE; Van Bergen, N; Davidson, KC; Anjomani Virmouni, S; Mckelvie, PA; Chrysostomou, V; Conquest, A; Corben, LA; Pook, MA; Kulkarni, T; Trounce, IA; Pera, MF; Delatycki, MB; Pébay, A |
| 2014 | Cellular, molecular and functional characterisation of YAC transgenic mouse models of Friedreich Ataxia | Virmouni, SA; Sandi, C; Al-Mahdawi, S; Pook, MA |
| 2015 | Targeting lipid peroxidation and mitochondrial imbalance in Friedreich's ataxia | Abeti, R; Uzun, E; Renganathan, I; Honda, T; Pook, MA; Giunti, P |
| 2011 | Prolonged treatment with pimelic o-aminobenzamide HDAC inhibitors ameliorates the disease phenotype of a Friedreich ataxia mouse model | Sandi, C; Pinto, RM; Al-Mahdawi, S; Ezzatizadeh, V; Barnes, G; Jones, S; Rusche, JR; Gottesfeld, JM; Pook, MA |
| 2012 | The mismatch repair system protects against intergenerational GAA repeat instability in a Friedreich ataxia mouse model | Ezzatizadeh, V; Pinto, RM; Sandi, C; Sandi, M; Al-Mahdawi, S; Te Riele, H; Pook, MA |
| 2018 | Bone marrow transplantation stimulates neural repair in Friedreich's ataxia mice | Kemp, KC; Hares, K; Redondo, J; Cook, AJ; Haynes, HR; Burton, BR; Pook, MA; Rice, CM; Scolding, NJ; Wilkins, A |
| 19-Feb-2019 | The role of mitochondrial labile iron in Friedreich's ataxia skin fibroblasts sensitivity to ultraviolet A | Reelfs, O; Abbate, V; Cilibrizzi, A; Pook, MA; Hider, RC; Pourzand, C |
| 15-Aug-2016 | Lentivirus-meditated frataxin gene delivery reverses genome instability in Friedreich ataxia patient and mouse model fibroblasts | Khonsari, H; Schneider, M; Al-Mahdawi, S; Chianea, YG; Themis, M; Parris, C; Pook, MA; Themis, M |
| 8-Jan-2018 | Effect of diazoxide on Friedreich ataxia models | Santoro, A; Virmouni, SA; Paradies, E; Coa, VLV; Al-Mahdawi, S; Khoo, M; Porcelli, V; Vozza, A; Perrone, M; Denora, N; Taroni, F; Merla, G; Palmieri, L; Pook, MA; Marobbio, CMT |
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