Brunel University Research Archive(BURA) preserves and enables easy and open access to all
types of digital content. It showcases Brunel's research outputs.
Research contained within BURA is open access, although some publications may be subject
to publisher imposed embargoes. All awarded PhD theses are also archived on BURA.
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| Issue Date | Title | Author(s) |
|---|---|---|
| 19-Feb-2019 | The role of mitochondrial labile iron in Friedreich's ataxia skin fibroblasts sensitivity to ultraviolet A | Reelfs, O; Abbate, V; Cilibrizzi, A; Pook, MA; Hider, RC; Pourzand, C |
| 15-Aug-2016 | Lentivirus-meditated frataxin gene delivery reverses genome instability in Friedreich ataxia patient and mouse model fibroblasts | Khonsari, H; Schneider, M; Al-Mahdawi, S; Chianea, YG; Themis, M; Parris, C; Pook, MA; Themis, M |
| 8-Jan-2018 | Effect of diazoxide on Friedreich ataxia models | Santoro, A; Virmouni, SA; Paradies, E; Coa, VLV; Al-Mahdawi, S; Khoo, M; Porcelli, V; Vozza, A; Perrone, M; Denora, N; Taroni, F; Merla, G; Palmieri, L; Pook, MA; Marobbio, CMT |
| 12-Jul-2021 | Interruptions of the FXN GAA Repeat Tract Delay the Age at Onset of Friedreich’s Ataxia in a Location Dependent Manner | Nethisinghe, S; Kesavan, M; Ging, H; Labrum, R; Polke, JM; Islam, S; Garcia-Moreno, H; Callaghan, MF; Cavalcanti, F; Pook, MA; Giunti, P |
| 2015 | A novel GAA-repeat-expansion-based mouse model of Friedreich's ataxia. | Anjomani Virmouni, S; Ezzatizadeh, V; Sandi, C; Sandi, M; Al-Mahdawi, S; Chutake, Y; Pook, MA |
| 26-Jan-2023 | A new FRDA mouse model [Fxnnull:YG8s(GAA) > 800] with more than 800 GAA repeats | Kalef-Ezra, E; Edzeamey, FJ; Valle, A; Khonsari, H; Kleine, P; Oggianu, C; Al-Mahdawi, S; Pook, MA; Anjomani Virmouni, S |
| 13-Jun-2022 | Frataxin Deficit Leads to Reduced Dynamics of Growth Cones in Dorsal Root Ganglia Neurons of Friedreich’s Ataxia YG8sR Model: A Multilinear Algebra Approach | Mollá, B; Sáenz-Gamboa, JJ; Insuasty, E; de la Iglesia-Vaya, M; Pook, MA; Pallardó, FV; Palau, F; Gonzalez-Cabo, P |
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